Sprengel deformity
Sprengel deformity, initially documented by Eulenberg back in 1863, represents a congenital anomaly affecting the scapular and periscapular regions. This condition manifests as an elevated and inwardly rotated scapula, accompanied by inflexible periscapular tissues, which collectively limit the range of motion within the shoulder girdle and result in an observable aesthetic anomaly. While this deformity typically arises sporadically, there have been instances of familial occurrence. Notably, Sprengel shoulder often presents in conjunction with Klippel-Feil syndrome and various other congenital skeletal irregularities.
The diagnosis of Sprengel deformity can be reliably ascertained through anteroposterior X-ray imaging. However, in contemporary clinical practice, computed tomography and magnetic resonance scans, coupled with three-dimensional reconstructions, have gained prominence for detecting any concomitant abnormalities. This webinar serves as a comprehensive exploration of surgical interventions aimed at enhancing both functionality and the physical appearance of patients affected by this condition.
Speakers
- Jörge Bahm, MD